Pityriasis rubra pilaris
What is it?
Chronic disease that presents a familiar form that begins in childhood, of genetic cause, and one that manifests in adults, of unknown cause.
Characteristics and symptoms
The disease is characterized by the formation of red and scaly lesions, which are initially punctiform, with follicular distribution (one lesion in each pore) and which, through evolution, become joined, forming plaques.
A characteristic manifestation is the formation of small, hardened and rough bumps on the back of the fingers. It can also occur thickening of the skin of the palms and soles.
The disease progresses with periods of improvement and worsening. Lesions usually affect the scalp, face, trunk and limbs, but may reach the whole body.
In the adult form, there is a tendency to improvement of the lesions over the years, less common in the familial form.
The best results are obtained with oral retinoids, requiring medical supervision, as they can cause side effects. The drugs for local use only help the treatment. Severe and resistant cases may require medications used in chemotherapy.
- Pityriasis lichenoides
- Pityriasis rosea